Sökning: "Cystic fibrosis"

Visar resultat 6 - 10 av 89 avhandlingar innehållade orden Cystic fibrosis.

  1. 6. Immunological aspects on cystic fibrosis lung disease

    Författare :Malin Carlsson; Njurmedicin; []
    Nyckelord :MEDICIN OCH HÄLSOVETENSKAP; MEDICAL AND HEALTH SCIENCES; MEDICIN OCH HÄLSOVETENSKAP; MEDICAL AND HEALTH SCIENCES; transplantation; Immunology; serology; pyocyanin; mannan binding lectin; Pseudomonas aeruginosa; ANCA; Cystic fibrosis; bactericidal permeability increasing protein; Immunologi; serologi;

    Sammanfattning : In cystic fibrosis (CF) colonization of the airways with Pseudomonas aeruginosa is a major cause of deterioration and death. Host defence fails to clear the invading bacteria, which results in a chronic destructive inflammatory process. LÄS MER

  2. 7. Cystic fibrosis in adults. Diagnostic, epidemiologic and quality-of-life aspects

    Författare :Marita Gilljam; Göteborgs universitet; []
    Nyckelord :MEDICIN OCH HÄLSOVETENSKAP; MEDICAL AND HEALTH SCIENCES; Cystic fibrosis; Cystic fibrosis transmembrane conductance regulator; Pregnancy; Male infertility; Bronchoalveolar lavage; Quality of life; Questionnaire;

    Sammanfattning : Background: Cystic fibrosis (CF) is a severe hereditary disease. The type of mutation in the Cystic Fibrosis Transmembrane conductance Regulator (CFTR) gene will determine the degree of CFTR chloride channel malfunction. LÄS MER

  3. 8. Chloride transport and inflammation in cystic fibrosis airways

    Författare :Georgia Varelogianni; Godfried Roomans; Marie Johannesson; Ólafur Baldersson; Örebro universitet; []
    Nyckelord :Cystic fibrosis; CFTR; chloride efflux; N-acetylcysteine; ambroxol; duramycin; Nod-like receptors; cytokines; Medicin; Medicine;

    Sammanfattning : Cystic fibrosis (CF) is one of the most common lethal, autosomal recessive inherited diseases among Caucasians. It is caused by a mutation in the cystic fibrosis transmembrane conductance regulator (CFTR), a chloride channel activated by cyclic AMP. LÄS MER

  4. 9. Gastroduodenal epithelial transport in patients with cystic fibrosis

    Författare :Karin Edshage Hallberg; Göteborgs universitet; []
    Nyckelord :MEDICIN OCH HÄLSOVETENSKAP; MEDICAL AND HEALTH SCIENCES; MEDICIN OCH HÄLSOVETENSKAP; MEDICAL AND HEALTH SCIENCES; Cystic fibrosis; CFTR; intestinal motility; gastric secretion; IgA; Ussing chamber; intestinal permeability; genotype;

    Sammanfattning : Cystic fibrosis (CF) is an inherited disease where respiratory failure due to chronic lung infection is the major cause of death. A defective protein, cystic fibrosis transmembrane conductance regulator (CFTR) alters chloride epithelial transport. LÄS MER

  5. 10. Aspects on the Diverse Manifestations of Cystic Fibrosis

    Författare :Helga Elidottir; Lund Pediatrik; []
    Nyckelord :MEDICIN OCH HÄLSOVETENSKAP; MEDICAL AND HEALTH SCIENCES; Cystic fibrosis; Glucose tolerance; Diabetes; Liver disease; Continuous glucose monitoring; Oral glucose tolerance test; Lung function; Epidemiolgy; N1303K variant;

    Sammanfattning : .... LÄS MER